Nikaidoh Procedure for Situs Inversus and Transposition of Great Arteries with Ventricular Septal Defect and Pulmonary Stenosis

We present the case of a patient who underwent a Nikaidoh procedure for total correction of transposition of the great arteries (TGA), ventricular septal defect (VSD), and pulmonary stenosis (PS). A young girl, 2 years and 4 months of age, weighing 3400 g at birth, was diagnosed with TGA, VSD, patent ductus arteriosus (PDA), and left ventricular outflow tract obstruction (LVOTO), with valvular and subvalvular PS. Because of frequent cyanosis, she had received a right-sided modified Blalock-Taussig (mBT) shunt when she was 8 months old. The Nikaidoh procedure was used for total correction (aortic root translocation, LVOT enlargement, VSD patch repair, neoaorta and coronary button reimplantation, and neopulmonary artery reconstruction by monocusp valved autologous pericardial patch with the Lecompte maneuver). The patient’s postoperative course was uneventful, and she was discharged from the surgical intensive care unit 10 days after the operation.